Q56.1 Male pseudohermaphroditism, not elsewhere classified
Instructional Notes:
-
Q56.1
Description: Male pseudohermaphroditism, not elsewhere classified
Inclusion Term:
- 46, XY with streak gonads
- Male pseudohermaphroditism NOS
↓
-
Q56
Description: Indeterminate sex and pseudohermaphroditism
Exclude1:
- 46,XX true hermaphrodite (Q99.1)
- androgen insensitivity syndrome (E34.5-)
- chimera 46,XX/46,XY true hermaphrodite (Q99.0)
- female pseudohermaphroditism with adrenocortical disorder (E25.-)
- pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
- pure gonadal dysgenesis (Q99.1)
↓
-
Q50-Q56
Description: Congenital malformations of genital organs (Q50-Q56)
Exclude1:
- androgen insensitivity syndrome (E34.5-)
- syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)
↓
-
Q00-Q99
Description: Congenital malformations, deformations and chromosomal abnormalities
Exclude2:
- inborn errors of metabolism (E70-E88)
Notes:
- Codes from this chapter are not for use on maternal records